First described by the Swedish paediatrician, Björn Ivemark, (1925-2005), IS is a rare congenital heterotaxic disorder with lateralization anomalies [1]. It accounts for 1- 3% of all congenital heart defects, with an incidence of 1 in 10-20,000 live births. To date, about 200 cases have been reported in the literature, mostly sporadic, but familial occurrence has also been described, suggesting autosomal recessive inheritance, with a male preponderance.

Zampetti, A., Gnarra, M., Linder, D., Antuzzi, D., Cataldi, L., Tulli, A., Feliciani, C., Early-onset basal cell carcinoma in a case of Ivemark syndrome, <<EUROPEAN JOURNAL OF DERMATOLOGY>>, 2010; 20 (6): 845-846. [doi:10.1684/ejd.2010.1093] [http://hdl.handle.net/10807/42930]

Early-onset basal cell carcinoma in a case of Ivemark syndrome

Zampetti, Anna;Feliciani, Claudio
2010

Abstract

First described by the Swedish paediatrician, Björn Ivemark, (1925-2005), IS is a rare congenital heterotaxic disorder with lateralization anomalies [1]. It accounts for 1- 3% of all congenital heart defects, with an incidence of 1 in 10-20,000 live births. To date, about 200 cases have been reported in the literature, mostly sporadic, but familial occurrence has also been described, suggesting autosomal recessive inheritance, with a male preponderance.
2010
Inglese
Zampetti, A., Gnarra, M., Linder, D., Antuzzi, D., Cataldi, L., Tulli, A., Feliciani, C., Early-onset basal cell carcinoma in a case of Ivemark syndrome, <<EUROPEAN JOURNAL OF DERMATOLOGY>>, 2010; 20 (6): 845-846. [doi:10.1684/ejd.2010.1093] [http://hdl.handle.net/10807/42930]
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/10807/42930
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