Identificador para citar o enlazar este ítem: http://hdl.handle.net/20.500.13003/17088
Idiopathic Pulmonary Fibrosis: Epidemiology, Natural History, Phenotypes.
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ISSN: 2076-3271
Scopus EID: 2-s2.0-85149155256
PMID: 30501130
Embase PUI: L640463172
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2018Tipo de documento
review articleCitación
Sauleda J, Nunez B, Sala E, Soriano JB. Idiopathic Pulmonary Fibrosis: Epidemiology, Natural History, Phenotypes.. Med Sci (Basel). 2018;6(4). 2018 Nov 29.Resumen
Idiopathic pulmonary fibrosis (IPF) is the most common of the idiopathic interstitial pneumonias. It is characterized by a chronic, progressive, fibrotic interstitial lung disease of unknown cause that occurs primarily in older adults. Its prevalence and incidence have appeared to be increasing over the last decades. Despite its unknown nature, several genetic and environmental factors have been associated with IPF. Moreover, its natural history is variable, but could change depending on the currently suggested phenotypes: rapidly progressive IPF, familial, combined pulmonary fibrosis and emphysema, pulmonary hypertension, and that associated with connective tissue diseases. Early recognition and accurate staging are likely to improve outcomes and induce a prompt initiation of antifibrotics therapy. Treatment is expected to be more effective in the early stages of the disease, while developments in treatment aim to improve the current median survival of 3⁻4 years after diagnosis.
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https://dx.doi.org/10.3390/medsci6040110Palabras clave
comorbiditiesevolution
idiopathic pulmonary fibrosis
incidence
prevalence
risk factors
Colecciones de Docusalut en las que aparece este ítem
Hospital Universitario Son Espases - HUSE > Comunicación científicaInstituto de Investigación Sanitaria Islas Baleares - IDISBA > Comunicación científica