Utilize este identificador para referenciar este registo:
http://hdl.handle.net/10400.16/1974
Título: | Spontaneous Dissection of the Renal Artery in Vascular Ehlers-Danlos Syndrome |
Autor: | Pereira, F. Cardoso, T. Sá, P. |
Data: | 2015 |
Editora: | Hindawi Publishing Corporation |
Citação: | Case Rep Crit Care. 2015;2015:804252 |
Resumo: | Ehlers-Danlos syndrome (EDS) is a rare heterogeneous group of connective tissue disorders. The vascular type (vEDS) is an autosomal dominant disorder caused by heterozygous mutations in the COL3A1 gene predisposing to premature arterial, intestinal, or uterine rupture. We report a case of a 38-year-old woman with a recent diagnosis of vEDS admitted in the Emergency Department with a suspicion of a pyelonephritis that evolved to a cardiopulmonary arrest. A fatal retroperitoneal hematoma related with a haemorrhagic dissection of the right renal artery was found after emergency surgery. This case highlights the need to be aware of the particular characteristics of vEDS, such as a severe vascular complication that can lead to a fatal outcome. |
Peer review: | yes |
URI: | http://hdl.handle.net/10400.16/1974 |
DOI: | 10.1155/2015/804252 |
ISSN: | 2090-6420 |
Versão do Editor: | http://www.hindawi.com/journals/cricc/2015/804252/ |
Aparece nas colecções: | SCIP2 - Artigos publicados em revistas indexadas na Pubmed/Medline SA - Artigos publicados em revistas indexadas na Pubmed/Medline |
Ficheiros deste registo:
Ficheiro | Descrição | Tamanho | Formato | |
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Spontaneous Dissection of the Renal Artery.pdf | 2,02 MB | Adobe PDF | Ver/Abrir |
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